Personalized External Aortic Root Support in Loeys Dietz Syndrome: Report of an Aortic Dissection at the Origin of the Right Coronary Artery

Sullivan KEO, McKendry A, Ball P and Graham ANJ

Department of Cardiothoracic Surgery, Royal Victoria Hospital, UK Departments of Radiology, Royal Victoria Hospital, Grosvenor Rd, UK

^*Correspondance to: Graham ANJ 

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Abstract:

Personalized external aortic root support is a novel therapy designed to wrap the aortic root externally to prevent progressive aneurysmal dilation in patients with connective tissue disorders such as Marfan syndrome. Histological investigation has revealed that it becomes integrated into the aortic adventitia thus providing additional strength. This procedure has been performed in 325 patients worldwide. Our centers established a PEARS program in 2016 and have undertaken 14 cases to date. We report an iatrogenic aortic dissection at the right coronary ostium in case 9 in our series in a patient with Elhers Danlos. We herein report this case to assist other centers considering PEARS and to disclose the important learning points encountered through our experience.

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Cite the Article:

Sullivan KEO, McKendry A, Ball P, Graham ANJ. Personalized External Aortic Root Support in Loeys Dietz Syndrome: Report of an Aortic Dissection at the Origin of the Right Coronary Artery. Ann Clin Case Rep. 2021; 6: 1918..