Kinsbourne Syndrome as the Unique Manifestation in Children with Neuroblastoma: Case Report

Sabbaga CC, Antunes LA, Talini C, Neves de Carvalho CB, Bersani Amado FA and Aranha Junior AA

Department of Pediatric Surgery, Hospital Pequeno Príncipe, Brazil

^*Correspondance to: César Cavalli Sabbaga 

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Abstract:

The opsoclonus-myoclonus-ataxia syndrome (OMAS) also known as Kinsbourne syndrome can occur as a single neurological event in children with paraneoplastic syndrome in a neuroblastoma low degree. This study aims to report a Kinsbourne syndrome in a 3 year-old-child and a literature review focused on the diagnosis and therapy alternatives. This report emphasizes the need for neurologists and pediatricians to suspect the hypothesis of an indolent neuroblastoma in patients presenting OMAS with no neuroimaging study changes. The high association with neuroblastoma is reported and should not be excluded even if a first investigation is negative. The patients high percentage with neurocognitive sequelae and permanent deficits is a challenge in the search for new and more aggressive treatment options.

Keywords:

Kinsbourne syndrome; Neuroblastoma; Opsoclonus-myoclonus-ataxia syndrome

Cite the Article:

Sabbaga CC, Antunes LA, Talini C, Neves de Carvalho CB, Bersani Amado FA, Aranha Junior AA. Kinsbourne Syndrome as the Unique Manifestation in Children with Neuroblastoma: Case Report. Ann Clin Case Rep. 2016; 1: 1042.