A Rare Cause of Large Cervical Spinal Cord Edema in the Absence of an Intramedullary Mass: Primary Diffuse Leptomeningeal Glioneuronal Tumor

Nermin Tepe1*, İbrahim Öztoprak2 and Gülay Turan3

1Department of Neurology, Balıkesir University, Turkey
2Department of Radiology, Canakkale Onsekiz Mart University, Turkey
3Department of Pathology, Balikesir University, Turkey

^*Correspondance to: Nermin Tepe 

 PDF  Full Text Case Report | Open Access

Abstract:

Introduction: Primary Diffuse Leptomeningeal Glioneuronal Tumor (DLGNT) is a rare tumor of the central nervous system. MRI of the tumor usually reveals diffuse leptomeningeal thickening, leptomeningeal contrast enhancement and hydrocephalus without any parenchymal lesion. In these patients, the predominant clinical findings are related to hydrocephalus. Spinal cord findings are more diverse than intracranial findings. Case Report: A 52-year-old female patient presented with a complaint of hydrocephalus. Her brain MRI showed hydrocephalus and diffuse hyperintense area between C2 and C7 in the spinal cord, consistent with edema. Conclusion: The diagnosis PDLG is difficult due to the variety of clinical findings and the rate of antemortem diagnosis is very low. We present a case with long segment cervical spinal cord edema without an intrinsic tumoral lesion, which is, as far as we know, not reported previously.

Keywords:

Cite the Article:

Tepe N, Öztoprak İ, Turan G. A Rare Cause of Large Cervical Spinal Cord Edema in the Absence of an Intramedullary Mass: Primary Diffuse Leptomeningeal Glioneuronal Tumor. Ann Clin Case Rep. 2022; 7: 2280..