Journal Basic Info

  • Impact Factor: 1.809**
  • H-Index: 6
  • ISSN: 2474-1655
  • DOI: 10.25107/2474-1655
**Impact Factor calculated based on Google Scholar Citations. Please contact us for any more details.

Major Scope

  •  ENT
  •  Cardio-Thoracic Surgery
  •  Molecular Biology
  •  Nephrology
  •  Anatomy
  •  Pulmonary Medicine
  •  Surgery Cases
  •  Physiology

Abstract

Citation: Ann Clin Case Rep. 2020;5(1):1853.DOI: 10.25107/2474-1655.1853

Association of Pediatric Rapunzel Syndrome with ProteinLosing Enteropathy

Johanna R Kaufman, Michelle Solomon and Seema Khan

Department of Graduate Medical Education, Children’s National Medical Center, USA George Washington School of Medicine, USA Kaiser MidAtlantic Permanente Medical Group, USA Division of Gastroenterology, Hepatology and Nutrition, Children’s National Medical Center, USA

*Correspondance to: Johanna R Kaufman 

 PDF  Full Text Case Report | Open Access

Abstract:

Rapunzel Syndrome describes the rare presentation of a trichobezoar with extension of ingested hairs through the pylorus into the small intestine. In this report, we describe the case of a 4-yearold girl presenting with anasarca found to have hypoalbuminemia, severe malnutrition and Protein-Losing Enteropathy (PLE). Further questioning revealed a history of trichotillomania and trichophagia. An upper GI series demonstrated findings of a trichobezoar extending into the proximal duodenum, consistent with Rapunzel Syndrome. An exploratory laparotomy with anterior gastrotomy removed an extensive trichobezoar. The patient subsequently tolerated advancement of diet with improvement in total serum protein levels. This signifies a rare presentation of PLE in the setting of Rapunzel Syndrome, as well as the youngest reported case of Rapunzel Syndrome to occur in the United States.

Keywords:

Cite the Article:

Kaufman JR, Solomon M, Khan S. Association of Pediatric Rapunzel Syndrome with Protein-Losing Enteropathy. Ann Clin Case Rep. 2020; 5: 1853.

Search Our Journal

Journal Indexed In

Articles in PubMed

Tocotrienols: Exciting Biological and Pharmacological Properties of Tocotrienols and other Naturally Occurring Compounds, Part I
 PubMed  PMC  PDF  Full Text
Tocotrienols: Exciting Biological and Pharmacological Properties of Tocotrienols and Naturally Occurring Compounds, Part II
 PubMed  PMC  PDF  Full Text
View More...

Articles with Grants

Clinical Course and Virus Shedding of Mild and Moderate COVID-19 in South China: A Retrospective Study
 Abstract  PDF  Full Text
Acute Portal Vein Thrombosis in Obesity: A Case Report and Review of Literature
 Abstract  PDF  Full Text
View More...